2024年11月17日 · People with PKU must adhere to a strict diet low in phenylalanine. This means avoiding high-protein foods such as meat, eggs, dairy products, nuts, and soybeans, as well as many common artificial sweeteners like aspartame, which contains phenylalanine.

The diet for PKU consists of a phenylalanine-free medical formula and carefully measured amounts of fruits, vegetables, bread, pasta, and cereals. Many people who follow a low phenylalanine (phe) food pattern eat special low protein breads and pastas.

2023年7月12日 · A PKU diet typically includes a phenylalanine-free medical formula or shake to meet your daily nutritional needs along with carefully measured amounts of fruits, vegetables, breads, pasta, and cereals to ensure you obtain just the …

2024年1月5日 · Following a low-Phe diet can reduce Phe levels and prevent intellectual disability and other neurological complications in people with phenylketonuria. Learn about foods to eat and foods to avoid.

2023年12月8日 · A phenylketonuria diet can include artificial protein substitutes. These substitutes derive from phenylalanine-free amino acids supplements. They may contain added carbohydrates, fats, and...

2017年4月24日 · Special phenylalanine-free foods are available for children and teens with PKU. The metabolic RDN will monitor and modify the customized eating plan as needed to promote healthy growth and development. The PKU-friendly diet needs to be followed for life to maintain serum phenylalanine levels, which will be checked during routine blood draws.

Aspartame (E951) is an artificial sweetener and 56% is converted to free phenylalanine and so should be excluded in a low phenylalanine diet. It is added to soft drinks, chewing gums, sweets, desserts, jelly and tabletop sweeteners.

The phenylalanine-free formula is the most important part of the diet for PKU. Another important part of the diet is low protein breads and pastas. They are nearly free of phenylalanine, allow greater freedom in food choices, and provide energy and variety in the diet.

Exchange-free foods are low in protein or phenylalanine. They can be eaten without weighing or measuring. Low protein prescription foods are low in protein or phenylalanine. They are an essential part of the diet providing energy and variety. …

In order to prevent neurological damage, lifelong adherence to a low-phe diet that is restricted in natural foods and requires ingestion of a phe-free AA formula to meet protein needs is required.