Although a diagnosis can usually be made without further investigation, other congenital melanocytic nevi can present in similar locations. A café-au-lait patch can present on the face, but its ...

Nevus of Ota, or nevus fuscoceruleus ophthalmomaxillaris, is a dermal melanocytic hamartoma that presents as bluish hyperpigmentation along the first or second branches of the trigeminal nerve.