Isovaleric Acidemia is treated with L-leucine restriction and supplemental glycine. Added glycine augments conversion of isovaleric acid (IVA) to isovalerylglycine (IVG) through glycine-N-acylase.

Body odour is usually associated with adults, particularly those going through puberty, but it can also be a concern in infants.While it is uncommon for babies to have persistent body odour, it does ...

Considering taking supplements to treat isovaleric acidemia? Below is a list of common natural remedies used to treat or reduce the symptoms of isovaleric acidemia. Follow the links to read common ...